Obliterative Bronchiolitis (OB) also known as Bronchiolitis Obliterans is a rare and life limiting form of non-reversible obstructive lung disease that occurs in children and adults after injury to the lower respiratory tract.
The small airways (bronchioles) are compressed and narrowed by fibrous (scar) tissue and inflammation and this can often lead to obstructive lung disease.s
Obliterative Bronchiolitis can be misdiagnosed as Asthma, Bronchiolitis, Pneumonia and Emphysema.
Mainly supportive, using anti-biotic, physiotherapy and sometimes oxygen therapy. Steroid and other inhalers have variable results. Surgery may be an option for a small number of patients. Lung transplants maybe an option in end-stage disease. Clinical course is very variable and prognosis for any individual is often difficult to predict.
Children with Obliterative Bronchiolitis can often have Bronchiectasis too. Bronchiectasis is an irreversible dilation or widening of the bronchiole tree (the branching tubes that carry air to the lungs). The bronchi are enlarged, inflamed and collapse easily. This means that the mucus that is normally carried away by tiny hairs (cilia) gets blocked. Mucus builds up and spills over into other tubes and these are more likely to be infected by bacteria. This then causes inflammation and damage called Bronchiectasis.
Although Breathtakers is intended primarily for suffers of OB much of the information on the support pages is generic and therefore may prove useful for sufferers of other rare lung disorders. As with OB there is often little information available and so hopefully this site may prove useful.
Adults can also suffer from ILD. The most common and severe form is interstitial pneumonia/ idiopathic pulmonary fibrosis, which has not been found in infants and young children. The term “Idiopathic Pulmonary Fibrosis” however means scarring of the lungs for unknown reasons, which can occur in children.